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Table 3 Reported Cases with Sites of Disease and Histologic Findings

From: Autoimmune enteropathy with a CD8+ CD7-T-cell small bowel intraepithelial lymphocytosis: case report and literature review

Reference

Gender, Age

Involved sites

Intra-epithelial

Lamina propria

16

F, 38

Small intestine

46%a

NR

16

F, 47

Small intestine

42%a

NR

8

F, 39

Stomach, duodenum, jejunum, colon, recto-sigmoid

12%a (normal), decreased CD3- CD103+, aberrant CD3+CD4+CD103-, increased HLA-II expression on CD3+

Lympho-plasmacytic infiltrate (CD3+)

19

F, 50

Duodenum, colon

Duodenum: IEL = 48/100, CD3 + 50/mm (elevated), eosinophils (some);

Colon: normal

Colon: lympho-plasmacytic infiltrate, eosinophils (some)

18

F, 82

Duodenum

Lympho-plasmacytic infiltrate

NR

20

M, 67

colon

NR

NR

20

F, 39

Small intestine, colon

NR

NR

22

F, 58

Stomach, duodenum, jejunum, colon, rectosigmoid

Duodenum: IEL = 10-20/100, CD8 + preponderance

Jejunum: lymphocytosis

Colon: chronic inflammation, CD4 + , CD8 + , CD19 + /20 + , CD68 +

Duodenum: CD3+ and CD43+ lymphocytosis with CD68 + (macrophages)

Jejunum: Inflammatory infiltrate

15

M, 54

Duodenum, ileum

Duodenum: IEL = 28/100 (normal), 50% CD8 + , oligoclonal TCR αβ +

Ileum: lymphocytosis

Colon: lymphocytosis

NR

3

M, 19

Duodenum, ileum, colon

Normal

NR

17

F, 35

Duodenum

IEL = > 40/100

52% CD3+

NR

21

M, 59

Stomach, colon, ileum

Normal

Colon + Ileum: lympho-plasmacytic infiltrate, occasional neutrophils and eosinophils

Stomach + Colon + Ileum: CD8 + and CD45RO + preponderance

4

M, 21

Duodenum

IEL = 50/100

CD8+ preponderance

CD4+ preponderance, occasional CD8+ and neutrophils, rare CD20+

24

M, 58

Duodenum, ileum, colon

Lymphocytosis

Lympho-plasmacytic infiltrate

  1. Abbreviations:
  2. IEL: Intra-epithelial lymphocytosis
  3. a: expressed as a percentage of total cells