Parameters | Total | Inactive PBC | Active PBC |
---|---|---|---|
n = 59 | n = 37 | n = 22 | |
Females (number) | 56 | 36 | 20 |
Males (number) | 3 | 1 | 2 |
Biochemical parameters: mean + SD (median) | |||
AP (U/l) (normal < 120) | 440 + 374 (309) | 344 + 250 (235) | 647+519 (537)a) |
ASAT (U/l) (normal < 35) | 38 + 43 (24) | 34 + 48 (20) | 46 + 28 (43)b) |
ALAT (U/l) (normal < 35) | 51 + 56 (26) | 43 + 53 (25) | 62 + 62 (42) |
γGT (U/l) (normal < 50) | 145 + 107 (129) | 128 + 86 (127) | 194 + 146 (164) |
bilirubin (mg%) (normal < 1.5) | 1,4 + 1,8 (1,0) | 0,8 + 0,7 (0,9) | 2,3 + 2,8 (1,5)b) |
IgG-globulins (mg%) (normal < 1800) | 1527 + 477 (1450) | 1395 + 603 (1310) | 1331 + 733 (1450) |
IgM-globulins (mg%) (normal < 280) | 373 + 201 (324) | 298 + 162 (162) | 398 + 290 (427) |
Histological stages (number): | |||
PBC I/II | 45 | 37 | 8 |
PBC III/IV | 14 | 0 | 14 |
Autoantibodies to: number (%) | |||
mitochondria (IFT) | 54 (92) | 33 (89) | 21 (95) |
M2 (ELISA) | 51 (86) | 31 (84) | 20 (91) |
nuclear dots (sp100; IFT) | 14 (24) | 9 (24) | 5 (23) |
nuclear membrane (gp210; IFT) | 4 (7) | 1 (3) | 3 (14) |
centromeres | 6 (10) | 2 (5) | 3 (14) |